Nurdan DİNLEN, İbrahim CANER, Kadir Ş. TEKGÜNDÜZ, Atilla ÇAYIR, Atilla TÜRKYILMAZ, Gülay DAL

Yenidoğanda Nadir Bir Solunum Sıkıntısı Nedeni: Konjenital Lober Amfizem

Konjenital lober amfizem akciğerin bir veya daha fazla lobunda hiperekspansiyon, kalan akciğerde kompresyon, mediastenin karşı tarafa kayması ile karakterize nadir gelişimsel bir anomalidir. Yenidoğan döneminde solunum sıkıntısına yol açmakla birlikte, ender olarak semptomların ortaya çıkışı altıncı aya kadar gecikebilir. Hafif olgularda konservatif tedavi tercih edilirken, solunum sıkıntısının düzelmediği olgularda cerrahi girişim gerekmektedir. Burada yenidoğan döneminde tanısı konularak lobektomi uygulanmış bir konjenital lober amfizem olgusu tartışılmıştır.

Anahtar Kelimeler:

Konjenital lober amfizem, Lobektomi, Solunum sıkıntısı, Yenidoğan

A Rare Cause of Respiratory Distress in the Newborn: Congenital Lobar Emphysema

Congenital lobar emphysema (CLE) is a rare malformation of lung development caused by the hyperinflation of the lung lobe with compression of the normal lung parenchyma and contralateral displacement of the mediastinum. It may represent immediately at birth with respiratory insufficiency or have a slower onset at 6 months of life. The treatment of choice may be conservative in mild cases or surgical removal of the affected lobe may be needed in severe cases that have persistent or progressive respiratory distress. A baby diagnosed as having CLE and whose affected lobe was surgically removed at the newborn period is presented and discussed

Keywords:

Congenital lobar emphysema, Lobectomy, Respiratory distress, Newborn,

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Yoshioka H, Aoyama K, Iwamura Y, Muguruma T, Kondo Y, Goto T, et al. Case of congenital lobar emphysema in an 18-month-old boy and review of earlier cases. Pediatr Int 2003;45:587-9.
Karnak I, Șenocak ME, Çiftçi OA, Büyükpamukçu N. Congenital Lobar emphysema: Diagnostic and therapeutic consideration. J Pediatr Surg 1999;34:1347-51.
Ozçelik U, Göçmen A, Kiper N, Doğru D, Dilber E, et al. Congenital lobar emphsema: Evaluation and long-term follow up thirty cases at a single centre. Pediatr Pulmonol 2003;35:384-91.
Karapurkar SA, Borkar JD, Birmole BJ. Malformation of lung in neonates (lobectomy for congenital lobar emphysema and lung cyst). J Postgrad Med 1993;39:224-7.
Kravitz RM. Congenital malformation of the lung. Pediatr Clin North Am 1994;41:453-72.
Sarioğlu T, Saylam A, Aytaç A, Sarikayalar F, Cağlar M, Alp M. Congenital lobar emphysema. Turk J Pediatr 1983;25:103–8.
Marleta Reynolds. Congenital lesions of the lung. In: Shilelds TW, Locicero III J, Ponn RB, (eds). General Thoracic Surgery. Philadelphia: Lippincott Williams & Wilkins, 2000: 940.
Doğan R, Demircin M, Sarıgül A, Paşaoğlu İ, Göçmen A, Bozer AY. Surgical management of congenital lobar emphysema. Turkish Pediatr 1997;39:35–44.
Lacy DE, Shaw NJ, Pilling DW, Walkinshaw S. Outcome of congenital lung abnormalities detected antenatally. Acta Paediatr 1999;88:454–8.
Markowitz RI, Mercurio MR, Vahjen AG, Gross I, Touloukian RJ. Congenital lobar emphysema the roles of CT and V/Q scan. Clin Pediatr 1989;28:19–23.
Gupta R, Singhal SK, Rattan KN, Chhabra B. Management of congenital lobar emphysema with endobronchial intubation and controlled ventilation. Anesth Analg 1998;86:71–3.