Ömer BEKTAŞ, Aydan DEĞERLİYURT, Cahide YILMAZ, Zeynep Kübra GÜRCAN, Alkım AKMAN ÖDEN, Bilge Dirce TAŞKIN, Esra ŞEKER DAĞ, Alev GÜVEN

Marcus Gunn Jaw Winking Sinkinezis: Konjenital Pitozisli İki Olgunun Sunumu

Marcus Gunn Jaw Winking Sinkinezis (MGJWS), levator palpebra superior kasının, trigeminal sinirin çiğneme kaslarını innerve eden motor dalı tarafından aberran olarak innerve edilmesi ile ortaya çıkan bir fenomendir. Konjenital pitozlu hastalar arasında %4-6 oranında saptanmaktadır. Genellikle tek taraflı ve izole olarak görülmekle beraber literatürde çok az sayıda bilateral ya da sistemik veya oküler anomalilerin eşlik ettiği olgular da bulunmaktadır. Biz de pitoz ile başvuran ve MGJWS tanısı alan iki olgudan bahsettik.

Anahtar Kelimeler:

Innervasyon hatası, Konjenital pitozis, Sinkinezi

Marcus Gunn Jaw Winking Synkinesis: Report of Two Cases with Congenital Ptosis

Marcus Gunn Jaw Winking Synkinedis (MGJWS) is caused by aberrant innervation of the levator palpebrae superioris muscle by a branch of the trigeminal nerve’s motor division that supplies mastication. This phenomenon is seen in 4 to 6% of congenital ptosis patients. MGJWS mostly occurs i an unilateral and isolated manner but it is less frequently bilateral and associated with ocular and systemic abnormalities. Here we describe two cases of children who presented with ptosis and were diagnosed with MGJWS

Keywords:

Innervational defect, Congenital ptosis, Synkinesis,

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