Kostmann Sendromu ve Ağ ız İ çi Bulğuları

Bu derlemede Kostmann Sendromu tanısı konulurken diş hekimlerinin öneminin sunulması amaçlandı. Nötrofiller akut enflamatuar yanıtta ve bakteriyel enfeksiyonlara karşı konak savunmasında kritik bir rol oynayan ve fagositoz yapan hücrelerdir. Nötropeni mutlak nötrofil sayısının 1.500/mm3 ’ün altına inmesi durumunda kullanılan terimdir. Mutlak nötrofil sayısı

Kostmann Syndrome and İntraoral Findinğs

In this review, it was aimed to present the importance of dentists in the diagnosis of Kostmann Syndrome. Neutrophils are cells that play a critical role in the acute inflammatory response and host defense against bacterial infections and cause phagocytosis. Neutropenia is the term used when the absolute neutrophil count falls below 1.500/mm3 . It is defined as Kostmann's syndrome when the absolute neutrophil count is

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