Savas DEMİRPENCE, Baris GUVEN, Ali YILDIRIM, Emin Alp ALAYUNT, Vedide TAVLİ

Hibrid yaklaşımı uygulanan hipoplastik sol kalp sendromlu iki olgu

Hipoplastik sol kalp sendromu; çoğunlukla sol ventrikül hipoplazisi veya atrezisi, mitral kapak hipoplazisi veya atrezisi ve çıkan aorta hipoplazisi veya atrezisini içeren doğumsal kalp defektleri spektrumunu kapsar. Hipoplastik sol kalp sendromu neonatal mortalitenin önemli bir nedenidir. Son yıllarda hibrid yaklaşımın popülaritesi artmıştır. Hibrid uygulama, pediyatrik kardiyolog ve kalp cerrahı arasında yakın işbirliği gerektiren, girişimsel kardiyoloji yaklaşımları ve cerrahi teknikleri birleştiren ve daha az invaziv olan birincil bir uygulamadır. Bu yazıda, hipoplastik sol kalp sendromu olan ve duktal stent ve iki taraflı pulmoner arter bantlamayı içeren hibrid yaklaşımı uygulanan iki olguyu sunduk.

Anahtar Kelimeler:

Bebek, yenidoğan, hipoplastik sol kalp sendromu, tedavi

Hybrid approach in two cases with hypoplastic left heart syndrome

Hypoplastic left heart syndrome (HLHS) encompasses a spectrum of congenital cardiac defects which mostly include left ventricular hypoplasia or atresia, mitral valve hypoplasia or atresia and ascending aortic hypoplasia and atresia. Hypoplastic left heart syndrome is a leading cause of neonatal mortality. In recent years, popularity of hybrid approach has increased. Hybrid procedures which requires close cooperations between paediatric cardiologists and cardiac surgeons includes a less invasive primary procedure; integrating interventional cardiology approaches and surgical techniques. Herein, we report two cases with hypoplastic left heart syndrome. We performed hybrid approach including ductal stenting and bilateral pulmonary banding on these patients.

Keywords:

Infant, newborn, hypoplastic left heart syndrome, treatment,

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