Serpil TUNA

Raynaud fenomeni\'ni taklit eden kompleks bölgesel ağrı sendromu tip 1

Kompleks Bölgesel Ağrı Sendromu Tip 1 (KBAS-1), tutulan ekstremite de şişlik, otonomik disfonksiyon ve distrofik değişiklikler ile karakterize kronik ağrılı bir sendromdur. Genellikle travma sonrası görülür, ama bazen travma olmadan da görülebilir. 14 yaşında kız çocuğunda, soğuk ve stresle aktive olan ve üst ekstremitede bilateral ve tekrarlayan ataklarla seyreden, Raynaud fenomenine benzer bir KBAS-1 saptadık. Bu olguyu, atipik seyirli olması ve nadir görülmesi nedeniyle literatür eşliğinde sunuyoruz.

Anahtar Kelimeler:

Kompleks bölgesel ağrı sendromu, refleks sempatik distrofi sendromu, Raynaud fenomeni

Complex regional pain syndrome type 1 mimicking Raynaud s phenomenon

Complex regional pain syndrome type 1 (CRPS-1) is a chronic pain syndrome characterized by severe pain, swelling, autonomic dysfunction and dystrophic changes in affected extremity. RSDS is a rare disease in children and usually occurs after trauma, however, without trauma may also occur. We were detected CRPS-1 activated by cold and stress and characterized by recurrent attacks in the bilateral upper extremities in 14 year-old girl, which is similar to Raynaud's phenomenon. We present this case with the literature because of its rarity and atypical course.

Keywords:

Complex regional pain syndrome, reflex sympathetic dystrophy syndrome, Raynaud\'s phenomenon,

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