SERPİL TUNA, Nilüfer BALCI

Raynaud fenomeni'ni taklit eden kompleks bölgesel ağrı sendromu tip 1

Kompleks Bölgesel Ağrı Sendromu Tip 1 (KBAS-1), tutulan ekstremite de şişlik, otonomik disfonksiyon ve distrofik değişiklikler ile karakterize kronik ağrılı bir sendromdur. Genellikle travma sonrası görülür, ama bazen travma olmadan da görülebilir. 14 yaşında kız çocuğunda, soğuk ve stresle aktive olan ve üst ekstremitede bilateral ve tekrarlayan ataklarla seyreden, Raynaud fenomenine benzer bir KBAS-1 saptadık. Bu olguyu, atipik seyirli olması ve nadir görülmesi nedeniyle literatür eşliğinde sunuyoruz.

Complex regional pain syndrome type 1 mimicking Raynauds phenomenon

Complex regional pain syndrome type 1 (CRPS-1) is a chronic pain syndrome characterized by severe pain, swelling, autonomic dysfunction and dystrophic changes in affected extremity. RSDS is a rare disease in children and usually occurs after trauma, however, without trauma may also occur. We were detected CRPS-1 activated by cold and stress and characterized by recurrent attacks in the bilateral upper extremities in 14 year-old girl, which is similar to Raynauds phenomenon. We present this case with the literature because of its rarity and atypical course.

PDF

___

1. Borchers AT, Gershwin ME. Complex regional pain syndrome: A comprehensive and critical reviewd. Autoimmun rev 2014;13:242-265.

2. Badri T, Ben Jennet S, Fenniche S. Reflex sympathetic dystrophy syndrome in a child. Acta Dermatovenerol Alp Pannonica Adriat 2011;20:77-79.

3. Shah J, Billington AR, Elston JB, Payne WG. Raynaud's Phenomenon. Eplasty 2013;13:ic58.

4. Harden RN, Bruehl S, Galer BS, et al. Complex regional pain syndrome: are the IASP diagnostic criteria valid and sufficiently comprehensive? Pain 1999;83:211-219.

5. Sherry DD, Weisman R. Psychologic aspects of childhood reflex neurovascular dystrophy. Pediatrics 1988;81:572-578.

6. Coderre TJ, Bennett GJ. A hypothesis for the cause of complex regional pain syndrome-type I (reflex sympathetic dystrophy): pain due to deep-tissue microvascular pathology. Pain Med 2010;11:1224-1238.

7. Herrick A, el-Hadidy K, Marsh D, Jayson M. Abnormal thermoregulatory responses in patients with reflex sympathetic dystrophy syndrome. J Rheumatol 1994;21:1319-1324.