RESUL YILMAZ, RUHİYE REİSLİ, Osman Mücahit TOSUN, Ahmet TOPAL, SEMA TUNCER UZUN

Limb-Girdle Musküler Distrofi’li Gebede Anestezi Yönetimi

Limb-girdle musküler distrofiler (LGMD), otozomal dominant veya resesif geçiş özelliği gösteren, pelvis ve omuz çevresi kaslarında ilerleyici zayıflık ve atrofi ile ortaya çıkan, heterojen bir hastalık grubudur. Rejyonal anestezi sezeryan operasyonları için hem anne açısından hem de bebek açısından birçok avantajlara sahip olmakla birlikte, kas hastalığı öyküsü bulunan hastalarda rejyonal anestezi uygulaması ile etkin bir anestezi sağlanabilmektedir. Bununla birlikte, genel anestezinin bu hastalar için öngörülen komplikasyonlarından uzak durmak da olasıdır. LGMD sık görülmemekle birlikte, anestezi yönetimi açısından özellikli noktalar içermektedir. Bu olguda, LGMD’li gebede anestezi yönetimimize ait klinik deneyimimizi sunmayı amaçladık.

Anesthetic Management of A Pregnant Woman With Limb-Girdle Muscular Dystrophy

Limb-girdle muscular dystrophies (LGMDs) are a group of heterogeneous diseases which are autosomal dominant or recessively inherited, and characterized with a progressive weakness and atrophy around the pelvis and in muscles of the shoulder. Not only has regional anesthesia many advantages both for the mother and the baby during C-section procedures but it may also provide effective anesthesia for patients with a history of muscular diseases. Moreover, it is possible to evade foreseeable complications of general anesthesia for such patients as well. Although LGMD is not common, it has specific anesthesia management issues. In this case, we aimed to present our clinical experience in a pregnant women with LGMD.

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